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Non-operative management of a splenic laceration in a patient with the Proteus syndrome.
  1. W Ceelen,
  2. J De Waele,
  3. M Kunnen,
  4. B de Hemptinne
  1. Department of Surgery, University Hospital, Gent University Medical School, Belgium.

    Abstract

    An adult patient with the Proteus syndrome sustained a grade III splenic laceration after falling off a horse. Clinical features of this rare disorder include subcutaneous and visceral hamartomatous tumours. The patient also suffered from chronic intravascular coagulation associated with extensive haemangiomatosis (Kasabach-Merritt syndrome). Considering the visceral anomalies and abnormal coagulation, a non-operative approach was preferred despite considerable transfusion requirement, and the patient successfully underwent embolisation of the splenic artery. This is the first reported case of splenic injury in a patient with Proteus syndrome.

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